Work in progress. This guide is being written and reviewed.

Understanding pulmonary hypertension

Educational, not medical advice. If you have an urgent concern, call your physician or 911.

Module 3 — Delivery and the NICU · Episode 11

What it is

Pulmonary hypertension is high blood pressure in the blood vessels of the lungs. In CDH, the lung vessels are fewer and more reactive, so it is hard for blood to flow through them and pick up oxygen. This is often the single biggest challenge in the early NICU course.

Why it matters

When lung-vessel pressure is high, blood can bypass the lungs and the baby’s oxygen levels drop. Managing this pressure is frequently the main day-to-day task of the team in the first weeks.

How it is managed

Approaches may include careful ventilation, medicines that relax the lung blood vessels, support for the heart and blood pressure, and avoiding triggers that worsen the pressure. Pulmonary hypertension can rise and fall over days, so the plan is adjusted continually. In the most severe cases, when oxygen cannot be maintained, ECMO may be needed, which the next episodes cover.

What to expect emotionally

Good days and harder days are common as pressures fluctuate. A setback does not necessarily mean a worse outcome; it is often part of the expected up-and-down course.


Next in Module 3: When ECMO is needed · Back to Module 3